Abstract
The segmental approach to the diagnosis of congenital heart disease (Van Praagh 1984) includes the following analysis:
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1.
What is the anatomic type of the three major cardiac segments: the viscero-atrial situs, the ventricles, and the great arteries? Consider the example of a patient with complete transposition (d-TGA) with VSD and pulmonary stenosis. The cardiac segments are: situs solitus of the atria and viscera, d-looping of the ventricles (morphologic right ventricle lies to the right of the morphologic left ventricle), and d-malposition of the great arteries (aortic valve annulus lies to the right of the pulmonary annulus).
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2.
How is each segment connected to the adjacent segment? In the example of d-TGA described above, there is atrioventricular concordance and ventriculoarterial discordance.
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3.
What are the associated malformations? In the example described above, the patient also has a conoventricular VSD and pulmonary valve stenosis associated with d-TGA.
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4.
How do the segmental combinations and connections, along with the associated malformations, function? The patient with the morphology described above will have cyanosis and reduced pulmonary blood flow.
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Krishnamurthy, R., Chung, T. (2008). Pediatric Cardiac MRI. In: Lucaya, J., Strife, J.L. (eds) Pediatric Chest Imaging. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-32676-2_15
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