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Intracranial epithelioid hemangioendothelioma

  • Case Report
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Abstract

Introduction

Epithelioid hemangioendothelioma (EHE) is an uncommon soft-tissue vascular neoplasm. Although a well-defined entity outside the neuraxis, its intracranial occurrence is rare. Literature review revealed 35 reported cases till date.

Case report

The authors report a case of intracranial EHE in a 15-year-old girl, who presented with a short history and unusual radiology. Following radical removal, the lesion recurred within 1 month and progressed to terminal stages. This tumor is thought to have an indolent intermediate malignancy potential and such rapid progression has not been reported so far.

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Acknowledgment

Authors greatfully acknowledge the help of Dr Ramaswamy MD (Pathology), for providing help with the details of the hispathology.

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Authors and Affiliations

  1. Post Graduate Institute of Neurological Surgery, ALNC, VHS Hospital, Taramani, Chennai, 600 113, India

    Murali Mohan S., Nigel Peter Symss, Anil Pande, Vasudevan M. Chakravarthy & Ravi Ramamurthi

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  1. Murali Mohan S.
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  2. Nigel Peter Symss
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  3. Anil Pande
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  4. Vasudevan M. Chakravarthy
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  5. Ravi Ramamurthi
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Correspondence to Murali Mohan S..

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Mohan S., M., Symss, N.P., Pande, A. et al. Intracranial epithelioid hemangioendothelioma. Childs Nerv Syst 24, 863–868 (2008). https://doi.org/10.1007/s00381-008-0634-4

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  • DOI: https://doi.org/10.1007/s00381-008-0634-4

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