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Epithelioid Hemangioendothelioma of the Mastoid Bone with Extension of Middle Cranial Fossa: A Case Report

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Abstract

Epithelioid hemangioendothelioma (EHE) is a rare sarcoma of vascular origin. It is frequently seen in the liver, lungs and bones. Cases with mastoid bone and intracranial extension are rarer. A 40 year old male, presented with a history of progressive headaches and a mass in the postauricular region for a duration of three months. Computer tomography of the temporal bone showed an approximately 40 × 30 mm soft tissue with osteolytic bony changes located in the mastoid bone. Epithelioid hemangioendothelioma is a rare sarcoma of vascular origin. Surgery is the first line of therapy. Prognosis is generally good, and may be better for primary intracranial disease than that for EHE originating elsewhere.

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Funding

This study did not receive any specific grant from fundig agencies in the public, commercial, or not-for-profit sectors.

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Authors and Affiliations

  1. Department of Otolaryngology, Liv Hospital Ankara, Ankara, Turkey

    Hatice Secil Akyildiz, Taylan Gun & Bahar Kayahan Sirkeci

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  1. Hatice Secil Akyildiz
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  2. Taylan Gun
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  3. Bahar Kayahan Sirkeci
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Contributions

Conception: HSA, TG; Design: HSA, TG, BKS; Data collection and/or Processing: TG, HSA; Analysis and/or İnterpretation: BKS, HSA, TG; Literature Review: HSA, TG; BKS; Writing Manuscript: HSA, TG; Critical Review: HSA, TG, BKS.

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Correspondence to Hatice Secil Akyildiz.

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Our study includes data from one human participiant, and the patient’s consent was obtained. The datasets used and/or analysed during the current study are available from the corresponding author on reasonable request.

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Akyildiz, H.S., Gun, T. & Kayahan Sirkeci, B. Epithelioid Hemangioendothelioma of the Mastoid Bone with Extension of Middle Cranial Fossa: A Case Report. Indian J Otolaryngol Head Neck Surg 75, 4050–4053 (2023). https://doi.org/10.1007/s12070-023-03954-4

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  • DOI: https://doi.org/10.1007/s12070-023-03954-4

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