Abstract
Retroperitoneal primitive neuroectodermal tumour is an uncommon disease. The main treatment consists of surgical resection, which can require resection of great vessels, depending on the location. We present a single case of a 19-year-old male with a large tumour. To achieve R0 resection we needed to remove the vena cava. Venous flow reconstruction was performed with a cava prosthesis.
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Horowitz M, DeLaney T, Malawer M, Tsokos M (1993) Ewing sarcoma family tumors: Ewing sarcoma of bone and soft tissue and the peripheral primitive neuroectodermal tumors. In: Pizzo P, Poplack D (eds) Principles and practice of pediatric oncology, 2nd Edn. Lippincott, Philadelphia, pp 115–152
Minana B, Fernandez T, Carrero V et al (1993) Abdominal paragangliomas. The experience of the Hospital 12 de Octubre. Actas Urol Esp 17:555–568
Sano H, Bonadio J, Gerbing RB et al (2006) International neuroblastoma pathology classification adds independent prognostic information beyond the prognostic contribution of age. Eur J Cancer 42:1113–1119
Storm FK, Mahvi DM (1991) Diagnosis and management of soft tissue sarcoma. Ann Surg 214:2–10
Chef C, Reid R, O’Dwyer PJ (2007) Value of biopsy in the assessment of a retroperitoneal mass. Surgeon 4:79–81
McHugo K (2007) Renal and adrenal tumours in children. Cancer Imaging 7:41–51
Thacker MM, Temple HT, Scully SP (2005) Current treatment for Ewing’s sarcoma. Expert Rev Anticancer Ther 5:319–331. Review
Kovar H (2003) Ewing tumour biology: perspectives for innovative treatment approaches. Adv Exp Med Biol 532:27–37
Swanson PE, Jaszcz W, Nakhleh RE et al (1992) Peripheral primitive neuroectodermal tumors. A flow cytometric analysis with immunohistochemical and ultrastructural observations. Arch Pathol Lab Med 116:1202–1208
Castelli P, Caronno R, Diffanetti G et al (2006) Surgical treatment of malignant involvement of the inferior vena cava. Int Semin Surg Oncol 16:3–19
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Álvarez-Laso, C., Azcano, E., González, J. et al. Primitive neuroectodermal peripheral tumour of the retroperitoneum. Clin Transl Oncol 10, 380–382 (2008). https://doi.org/10.1007/s12094-008-0217-6
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DOI: https://doi.org/10.1007/s12094-008-0217-6