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An unusual case of duodenal obstruction-gangliocytic paraganglioma

  • Case report of interest
  • Published:
Journal of Hepato-Biliary-Pancreatic Surgery

Abstract

Gangliocytic paragangliomas are rare tumors located in the gastrointestinal tract that are considered to be benign. They are composed of spindle-shaped cells, epithelioid cells, and ganglion-like cells. They usually present with abdominal pain, and/or gastrointestinal bleeding, and occasionally with obstructive jaundice. We report a case of obstruction in a 17-year-old female, which on histology was found to be a gangliocytic paraganglioma, with an extremely unusual presentation. Intraoperatively, the patient was found to have local tumor extension and regional lymph node invasion, and so she underwent a pylorus-preserving pancreaticoduodenectomy, with local lymph node clearance. We discuss the management of this unusual case and review the literature.

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Authors and Affiliations

  1. West Midlands Liver Unit, Queen Elizabeth Hospital, University Hospital Birmingham NHS Foundation Trust, Birmingham, B15 2TH, UK

    C. M. Mann, S. R. Bramhall, J. A. Buckels & P. Taniere

Authors
  1. C. M. Mann
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  2. S. R. Bramhall
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  3. J. A. Buckels
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  4. P. Taniere
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Corresponding author

Correspondence to C. M. Mann.

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Mann, C.M., Bramhall, S.R., Buckels, J.A. et al. An unusual case of duodenal obstruction-gangliocytic paraganglioma. J Hepatobiliary Pancreat Surg 16, 562–565 (2009). https://doi.org/10.1007/s00534-009-0092-8

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  • DOI: https://doi.org/10.1007/s00534-009-0092-8

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