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Fahr's syndrome: local inflammatory factors in the pathogenesis of calcification

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Summary

Three cases of Fahr's syndrome are described. All patients had disturbances of calcium metabolism and had had a meningoencephalitis in childhood. It is suggested that gliovascular changes, induced by cerebral inflammation, can later facilitate the occurrence of calcification of the striopallidodentate system when abnormality of calcium metabolism develops.

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Morgante, L., Vita, G., Meduri, M. et al. Fahr's syndrome: local inflammatory factors in the pathogenesis of calcification. J Neurol 233, 19–22 (1986). https://doi.org/10.1007/BF00313985

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  • DOI: https://doi.org/10.1007/BF00313985

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