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Augenmanifestationen bei Churg-Strauss-Syndrom

Übersichtarbeit und Fallvorstellung

Ocular manifestations of Churg-Strauss syndrome

Review article and case report

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Zusammenfassung

Diese Arbeit fasst mögliche okuläre Manifestationen bei Churg-Strauss-Syndrom (CCS) in der Literatur zusammen und präsentiert eine ungewöhnliche Fallvorstellung aus dem klinischen Alltag mit konjunktivalen Granulomen, Pseudotumor orbitae und Aderhautfalten. CSS ist eine ANCA-assoziierte granulomatöse Vaskulitis, die sich in verschiedenen Organen manifestieren kann und eine lebensbedrohliche Situation für die Patienten darstellt. Okuläre Manifestationen sind selten und können sich auf alle Segmente des Auges und der Orbita ausbreiten. Die häufigsten beschriebenen Augenbeteiligungen in der Literatur sind retinale Verschlüsse und der Pseudotumor orbitae verschiedener Ausprägung.

Abstract

This paper summarizes the possible ocular manifestations of Churg-Straus syndrome (CCS) from the literature and presents an unusual case report from routine clinical practice with conjunctival granuloma, orbital pseudotumor and choroidal folds. The CSS is an ANCA-associated granulomatous vasculitis which can be manifested in various organs and represents a life-threatening situation for the patient. Ocular manifestations are rare and can spread to all segments of the eye and orbit. The most frequent forms of ocular involvement described in the literature are retinal occlusion and orbital pseudotumor with various degrees of expression.

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Authors and Affiliations

  1. Bereich Strabologie und Neuroophthalmologie, Augen-Praxis-Klink Esslingen, Adlerstr. 6, 73728, Esslingen, Deutschland

    A. Atili

  2. Abteilung für Nephrologie und Rheumatologie, Zentrum Innere Medizin, Universitätsmedizin Göttingen, Göttingen, Deutschland

    C. Richter

  3. Institut für Neuropathologie, Universitätsmedizin Göttingen, Göttingen, Deutschland

    E. Bahn

  4. Abteilung für Neuroradiologie, Universitätsmedizin Göttingen, Göttingen, Deutschland

    H.H. Rustenbeck

  5. Abteilung Augenheilkunde, Universitätsmedizin Göttingen, Bereich Strabologie, Neuroophthamologie und okuloplastische Chirurgie, Göttingen, Deutschland

    M. Schittkowski

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  1. A. Atili
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  2. C. Richter
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  3. E. Bahn
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Atili, A., Richter, C., Bahn, E. et al. Augenmanifestationen bei Churg-Strauss-Syndrom. Ophthalmologe 110, 1051–1057 (2013). https://doi.org/10.1007/s00347-013-2815-0

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