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Churg–Strauss syndrome complicated by central retinal artery occlusion: case report and a review of the literature

  • Case Report
  • Published:
Modern Rheumatology

Abstract

A 68-year-old man was admitted with rapid visual loss. Churg–Strauss syndrome (CSS) was diagnosed, based upon the symptoms of asthma, eosinophilia, interstitial pneumonitis, and positive myeloperoxidase-anti neutrophil cytoplasmic antibody (MPO-ANCA). Light reflexes were absent and vision was completely lost in both eyes. Bilateral central retinal artery occlusion (CRAO) was observed by fluorescence angiography. Steroid pulse along with an anticoagulant improved the visual acuity to light perception and hand motion. CSS-associated CRAO should be considered when acute visual loss occurs.

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Authors and Affiliations

  1. Department of Internal Medicine, Teikyo University School of Medicine, 2-11-1 Kaga, Itabashi-ku, Tokyo, 173-8605, Japan

    Kurumi Asako, Maki Takayama & Hajime Kono

  2. Department of Microbiology and Immunology, Teikyo University School of Medicine, 2-11-1 Kaga, Itabashi-ku, Tokyo, 173-8605, Japan

    Hirotoshi Kikuchi

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  1. Kurumi Asako
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  2. Maki Takayama
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  3. Hajime Kono
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  4. Hirotoshi Kikuchi
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Correspondence to Hirotoshi Kikuchi.

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Asako, K., Takayama, M., Kono, H. et al. Churg–Strauss syndrome complicated by central retinal artery occlusion: case report and a review of the literature. Mod Rheumatol 21, 519–523 (2011). https://doi.org/10.1007/s10165-011-0422-y

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  • DOI: https://doi.org/10.1007/s10165-011-0422-y

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