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Macronutrient Requirements

  • Chapter
Nutrition in Cystic Fibrosis

Part of the book series: Nutrition and Health ((NH))

Abstract

The wide array of clinical manifestations of cystic fibrosis (CF) leads to the conclusion that nutrient needs will be as equally variable. Many individuals with CF will likely require higher nutrient intakes in order to overcome losses in the stool and to achieve expected growth or weight gain/maintenance. Sicker patients in particular might demonstrate extremely high calorie needs. Others may do well on a level of calorie and nutrient intake that is considered normal. Calorie needs will be best determined by each individual’s current intake as well as their clinical and nutritional status. Patients, especially those with high energy needs, may benefit from a diet higher in fat (approximately 35 % of total calories) than is recommended for the standard population. Protein is an important nutrient to prevent catabolism; recommended intakes are 1.5–2 times greater than the recommended daily allowance or 15 % of total calories. There are no specific recommendations for carbohydrate provision and intake is generally adequate in people with CF.

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Authors and Affiliations

  1. Department of Nutrition and Food Services, UCSF Benioff Children’s Hospital San Francisco, 1855 4th Street, San Francisco, CA, 94143, USA

    Jaclyn Brownlee R.D., C.N.S.C.

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  1. Jaclyn Brownlee R.D., C.N.S.C.
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Correspondence to Jaclyn Brownlee R.D., C.N.S.C. .

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  1. Department of Pediatrics, Division of Gastroenterology, Hepatology and Nutrition, University of California, San Francisco, San Francisco, California, USA

    Elizabeth H. Yen

  2. Gastorenterology and Nutrition, The Johns Hopkins Children’s Center, Baltimore, Maryland, USA

    Amanda Radmer Leonard

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Brownlee, J. (2015). Macronutrient Requirements. In: Yen, E., Leonard, A. (eds) Nutrition in Cystic Fibrosis. Nutrition and Health. Humana Press, Cham. https://doi.org/10.1007/978-3-319-16387-1_2

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