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Acute Zonal Occult Outer Retinopathy (AZOOR)

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Encyclopedia of Ophthalmology

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Acute zonal occult outer retinopathy (AZOOR), initially described by Gass during the Donders’ Lecture in 1993 (Gass 1993), is a syndrome characterized by sudden unilateral or bilateral zonal loss of outer retinal function corresponding to visual field defects, photopsias, variable or limited funduscopic changes, and electroretinogram (ERG) abnormalities. Vitreous inflammation can develop in those eyes that suffer higher degrees of visual field loss, and involvement of the fellow eye can occur weeks or even several years after initial presentation. Affected patients occasionally complain of an antecedent viral illness and their symptoms persist for approximately 4–6 months, after which the visual field loss often stabilizes or slightly improves (Gass et al. 2002). Late recurrences and progression have been described in some patients (Gass et al. 2002).

Since its initial description, features of AZOOR have been described in patients with multifocal choroiditis and panuveitis (MFC),...

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Authors and Affiliations

  1. Vitreoretinal Diseases, Vanderbilt University School of Medicine, Vanderbilt Eye Institute, 2311, Pierce Avenue, Nashville, TN, 37232, USA

    Rohan J. Shah & Anita Agarwal

Authors
  1. Rohan J. Shah
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  2. Anita Agarwal
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Correspondence to Rohan J. Shah .

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Editors and Affiliations

  1. Dept of Ophthal & Optometry,AKH, Medical University of Wien Dept of Ophthal & Optometry,AKH, Wien, Austria

    Ursula Schmidt-Erfurth

  2. Department of Ophthalmology, Goethe University of Frankfurt am Main Department of Ophthalmology, Frankfurt am Main, Germany

    Thomas Kohnen

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Shah, R.J., Agarwal, A. (2014). Acute Zonal Occult Outer Retinopathy (AZOOR). In: Schmidt-Erfurth, U., Kohnen, T. (eds) Encyclopedia of Ophthalmology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-35951-4_985-1

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  • DOI: https://doi.org/10.1007/978-3-642-35951-4_985-1

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  • Online ISBN: 978-3-642-35951-4

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