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Malignant rhabdoid tumor: primary intracranial manifestation in an adult

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Summary

Clinical, histopathological, and ultrastructural features of an extended intracranial malignant neoplasm are presented. Following incomplete extirpation of a large epidural tumor at the temporal base of the skull, the 21-year-old male patient suffered from several local recurrences and died at the age of 27. The neoplasm was defined by its histopathological and ultrastructural characteristics and by the pattern of its antigenicity as a malignant rhabdoid tumor (MRT). Considering previous publications on MRT, this case may be the first of primary intracranial MRT appearing in an adult.

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Authors and Affiliations

  1. Neurologisches Institut (Edinger-Institut), Universität Frankfurt/Main, Deutschordenstrasse 46, W-6000, Frankfurt/Main, Germany

    M. Horn, W. Schlote & E. Thomas

  2. Neurochirurgische Klinik, Städtische Kliniken Dortmund, Münsterstrasse 240, W-4600, Dortmund, Germany

    K. D. Lerch

  3. Zentrum der Neurologie und Neurochirurgie, Universität Frankfurt/Main, Schleusenweg 2-16, W-6000, Frankfurt/Main, Germany

    W. I. Steudel

  4. Institut für Pathologie, Abteilung Paidopathologie, Universität Kiel, Michaelisstrasse 11, W-2300, Kiel, Germany

    D. Harms

Authors
  1. M. Horn
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  2. W. Schlote
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  3. K. D. Lerch
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  4. W. I. Steudel
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  5. D. Harms
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  6. E. Thomas
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Horn, M., Schlote, W., Lerch, K.D. et al. Malignant rhabdoid tumor: primary intracranial manifestation in an adult. Acta Neuropathol 83, 445–448 (1992). https://doi.org/10.1007/BF00713540

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  • DOI: https://doi.org/10.1007/BF00713540

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