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Kasabach–Merritt Syndrome

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Atlas of Genetic Diagnosis and Counseling

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Abstract

Kasabach–Merritt syndrome (or phenomenon) is the association of a vascular tumor and thrombocytopenic coagulopathy (Enjolras et al. 2000). It is a life-threatening, acute, or chronic consumptive coagulopathy, characterized by profound thrombocytopenia and microangiopathic hemolytic anemia (Esterly 1983).

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Authors and Affiliations

  1. Medical Genetics, Shriners Hospitals for Children, Shreveport, LA, USA

    Harold Chen

  2. Perinatal and Clinical Genetics, Department of Pediatrics, LSU Health Sciences Center, 1501 Kings Highway, 71130, Shreveport, LA, USA

    Harold Chen

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  1. Harold Chen
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Correspondence to Harold Chen .

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Chen, H. (2016). Kasabach–Merritt Syndrome. In: Atlas of Genetic Diagnosis and Counseling. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6430-3_139-2

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  • DOI: https://doi.org/10.1007/978-1-4614-6430-3_139-2

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  • Publisher Name: Springer, New York, NY

  • Online ISBN: 978-1-4614-6430-3

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