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Giant cavernous haemangioma with Kasabach-Merritt syndrome: a case report and review

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Abstract.

We report the case of a 4-month-old boy presenting with a giant cutaneous haemangioma complicated by Kasabach-Merritt syndrome (KMS) with severe thrombocytopenia. After poor response to corticosteroid therapy and subsequent treatment with interferon alpha-2a, radiotherapy led to tumour regression and resolution of the disseminated intravascular coagulopathy over a 14-month period of follow up. Whereas the various available treatment options are reviewed and discussed in this article, the therapy of choice should be chosen individually. Conclusion: to date prospective randomised and controlled trials are required to investigate the optimal management of patients with Kasabach-Merritt syndrome.

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Authors and Affiliations

  1. Department of Paediatrics, University Children's Hospital Münster, Albert-Schweitzer-Strasse 33, 48149 Münster, Germany, Germany

    Tanja Frevel, Heike Rabe, Frank Ückert & Erik Harms

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  1. Tanja Frevel
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  2. Heike Rabe
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  3. Frank Ückert
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  4. Erik Harms
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Correspondence to Tanja Frevel.

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Frevel, T., Rabe, H., Ückert, F. et al. Giant cavernous haemangioma with Kasabach-Merritt syndrome: a case report and review. Eur J Pediatr 161, 243–246 (2002). https://doi.org/10.1007/s00431-002-0953-5

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  • DOI: https://doi.org/10.1007/s00431-002-0953-5

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