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Polyzystische Nierenerkrankungen

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Monogen bedingte Erbkrankheiten 2

Part of the book series: Handbuch der Molekularen Medizin ((HDBMOLEK,volume 7))

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Zusammenfassung

Zystische Nierenkrankheiten spielen in vielen Bereichen der Medizin eine wichtige Rolle, etwa 5-10% der Dialysepatienten leiden an Zystennieren. Zystennieren stellen eine heterogene Gruppe dar, die sowohl erworbene als auch erbliche Formen einschließt (Zerres et al. 1984). Die Klassiflkation ist nicht einheitlich, zunehmend werden jedoch im klinischen Gebrauch die genetischen Bezeichnungen den pathoanatomischen vorgezogen, obwohl diese weiterhin für die Beschreibung der morphologischen Lßsionen von Bedeutung sind.

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  1. Klaus Zerres
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  2. Sabine Rudnik-Schöneborn
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Zerres, K., Rudnik-Schöneborn, S. (2000). Polyzystische Nierenerkrankungen. In: Ganten, D., Ruckpaul, K. (eds) Monogen bedingte Erbkrankheiten 2. Handbuch der Molekularen Medizin, vol 7. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-57044-5_9

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