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Medical Therapy for Chronic Right Ventricular Failure in Congenital Heart Disease

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Right Ventricular Physiology, Adaptation and Failure in Congenital and Acquired Heart Disease

Abstract

The clinical importance of right ventricular (RV) function has been increasingly recognised in populations with and without congenital heart disease (CHD). CHD patients most at risk of chronic RV failure are those with repaired tetralogy of Fallot (TOF), atrial baffle redirection procedures for transposition of the great arteries (TGA-baffle), congenitally corrected transposition of the great arteries (ccTGA), Ebstein anomaly of the tricuspid valve or a Fontan circulation with a dominant RV. This chapter considers medical management options that might be beneficial in these groups. It reviews current literature and guidelines, offers opinions based on clinical experience and discusses potential avenues for future research.

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Authors and Affiliations

  1. The Peter Munk Cardiac Center, University Health Network, Toronto Congenital Cardiac Center for Adults, 5N-521, 585 University Avenue, Toronto, ON, Canada, M5G 2N2

    S. Lucy Roche

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  1. S. Lucy Roche
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Correspondence to S. Lucy Roche .

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Editors and Affiliations

  1. Paediatric Cardiology, Labatt Family Heart Center Hospital for Sick Children, Toronto, Ontario, Canada

    Mark K. Friedberg

  2. Heart Institute, Cincinnati Children’s Hosp Med Center, Cincinnati, Ohio, USA

    Andrew N. Redington

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Roche, S.L. (2018). Medical Therapy for Chronic Right Ventricular Failure in Congenital Heart Disease. In: Friedberg, M., Redington, A. (eds) Right Ventricular Physiology, Adaptation and Failure in Congenital and Acquired Heart Disease. Springer, Cham. https://doi.org/10.1007/978-3-319-67096-6_16

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  • DOI: https://doi.org/10.1007/978-3-319-67096-6_16

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