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Born with a Failing Right Heart

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Clinical Cases in Right Heart Failure

Part of the book series: Clinical Cases in Cardiology ((CCC))

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Abstract

Tetralogy of Fallot is one of the most common congenital heart diseases with increasing numbers of patients surviving into adulthood due to advances in surgical and transcatheter techniques. Whereas children undergo surgical repair early, the pathophysiology has a lifetime of consequences, increasing the risk of right heart failure with variable timing and presentation throughout adulthood. Key sequelae of repair include pulmonary regurgitation, pulmonary stenosis, impaired right ventricular function, left ventricular dysfunction, arrhythmias, and conduction abnormalities—all of which contribute to morbidity and mortality later in life. These sequelae are managed using a combination of medical therapy, pacemaker and defibrillator devices, transcatheter and surgical valve replacement, and advanced heart failure therapies, including heart transplantation.

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Authors and Affiliations

  1. Department of Medicine, Division of Cardiology, Emory University School of Medicine, Atlanta, GA, USA

    Matthew R. Carazo & Maan Jokhadar

  2. Department of Cardiology, Boston Children’s Hospital, Boston, MA, USA

    Michael J. Landzberg

  3. Division of Cardiovascular Medicine, Brigham and Women’s Hospital, Boston, MA, USA

    Michael J. Landzberg

  4. Harvard Medical School, Boston, MA, USA

    Michael J. Landzberg

Authors
  1. Matthew R. Carazo
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  2. Michael J. Landzberg
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  3. Maan Jokhadar
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Corresponding author

Correspondence to Michael J. Landzberg .

Editor information

Editors and Affiliations

  1. St. Elizabeth’s Medical Center, Boston, MA, USA

    Lana Tsao

  2. Maine Medical Center, Portland, ME, USA

    Maxwell E. Afari

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Carazo, M.R., Landzberg, M.J., Jokhadar, M. (2020). Born with a Failing Right Heart. In: Tsao, L., Afari, M. (eds) Clinical Cases in Right Heart Failure. Clinical Cases in Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-030-38662-7_4

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  • DOI: https://doi.org/10.1007/978-3-030-38662-7_4

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-38661-0

  • Online ISBN: 978-3-030-38662-7

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