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Cardiomyopathies

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Cardiac Pathology

Abstract

The cardiomyopathies are a heterogeneous group of diseases centred on the myocardium. Most have an underlying genetic basis, although some may be secondary to other disorders. The main pathologies described in this chapter are dilated cardiomyopathy, hypertrophic cardiomyopathy, arrhythmogenic (right ventricular) cardiomyopathy, isolated left ventricular non-compaction and restrictive cardiomyopathy. The chapter provides macroscopic and microscopic descriptions of the various forms of cardiomyopathies and describes current concepts surrounding their diagnosis, pathogenesis and genetic background.

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Acknowledgements

Grateful thanks are expressed to Mr. B. Wagner, Senior Electron Microscopist, Sheffield Teaching Hospitals for his expertise and photography of ultrastructural histology in this chapter.

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  1. Royal Hallamshire Hospital, Sheffield, UK

    Clare R. Bunning

  2. Sheffield Teaching Hospitals, Royal Hallamshire Hospital Sheffield Teaching Hospitals Sheffield, South Yorkshire, UK

    S. Kim Suvarna

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  1. Sheffield Teaching Hospitals, Royal Hallamshire Hospital Sheffield Teaching Hospitals, Sheffield, South Yorkshire, UK

    S. Kim Suvarna

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Bunning, C.R., Suvarna, S.K. (2019). Cardiomyopathies. In: Suvarna, S. (eds) Cardiac Pathology. Springer, Cham. https://doi.org/10.1007/978-3-030-24560-3_11

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  • DOI: https://doi.org/10.1007/978-3-030-24560-3_11

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