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Associated Bony Malformations and Instability in the Chiari I Malformation

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The Chiari Malformations

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Abstract

The incidence of craniovertebral junction (CVJ) bony abnormalities in Chiari I malformations is between 7 and 11 %. However, the incidence of CVJ bony abnormalities having a hindbrain herniation is 33–38 %.

There are numerous bony abnormalities with Chiari I malformation in whom instability may be present. The commonest symptom is headache, centered in the base of the skull, often described as “heaviness of the head.” Nausea, extreme dizziness, and vasomotor instability are frequently present. This is corrected with stabilization with temporary brace or permanently with decompression and fusion.

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Authors and Affiliations

  1. Department of Neurosurgery, University of Iowa Hospitals and Clinics, 200 Hawkins Drive, 1824 JPP, Iowa City, IA, 52242, USA

    Arnold H. Menezes MD

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  1. Arnold H. Menezes MD
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Correspondence to Arnold H. Menezes MD .

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Editors and Affiliations

  1. Children's Hospital of Alabama, 7th Ave S 1600, Birmingham, 35233-1711, Alabama, USA

    R. Shane Tubbs

  2. The Children's Hospital of Alabama, 7th Ave S 1600, Birmingham, 35233-1711, Alabama, USA

    W. Jerry Oakes

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Menezes, A.H. (2013). Associated Bony Malformations and Instability in the Chiari I Malformation. In: Tubbs, R., Oakes, W. (eds) The Chiari Malformations. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6369-6_14

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  • DOI: https://doi.org/10.1007/978-1-4614-6369-6_14

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  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4614-6368-9

  • Online ISBN: 978-1-4614-6369-6

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