Abstract
Congenital infantile fibrosarcoma is a rare soft tissue malignancy that occurs in both axial and extremity locations. We report a case of this tumor arising from the left colon in a newborn presenting with an intrauterine perforation and meconium peritonitis.
References
Emil S, Nguyen T, Sills J et al (2004) Meconium obstruction in extremely low birth weight neonates: guidelines for diagnosis and management. J Pediatr Surg 39:731–737
Groff DB (2000) Meconium disease. In: Ashcraft KW, Murphy JP, Sharp RJ et al (eds) Pediatric surgery. WB Saunders, Philadelphia, pp 435–442
Eckoldt F, Heling KS, Woderich R et al (2003) Meconium peritonitis and pseudo-cyst formation: prenatal diagnosis and post-natal course. Prenat Diagn 23:904–908
Blocker S, Koenig J, Ternberg J (1987) Congenital fibrosarcoma. J Pediatr Surg 22:665–670
Coffin CM, Jaszcz W, O’Shea PA et al (1994) So-called congenital infantile fibrosarcoma: does it exist and what is it? Pediatr Pathol 14:133–150
Wilson MB, Stanley W, Sens D et al (1990) Infantile fibrosarcoma—a misnomer? Pediatr Pathol 10:901–907
Surico G, Muggeo P, Daniele RM et al (2003) Chemotherapy alone for the treatment of congenital fibrosarcoma: is surgery always needed? Med Pediatr Oncol 40:268–270
Pousti TJ, Upton J, Loh M et al (1998) Congenital fibrosarcoma of the upper extremity. Plast Reconstr Surg 102:1158–1162
Coffin CM, Dehner LP (1990) Soft tissue tumors in the first year of life: a report of 190 cases. Pediatr Pathol 10:509–526
Shima Y, Ikegami E, Takechi N et al (2003) Congenital fibrosarcoma of the jejunum in a premature infant with meconium peritonitis. Eur J Pediatr Surg 13:134–136
Fisher C (1996) Fibromatosis and fibrosarcoma in infancy and childhood. Eur J Cancer 32A:2094–2100
Numanoglu A, Davies J, Millar AJ, Rode H (2002) Congenital solitary intestinal fibromatosis. Eur J Pediatr Surg 12:337–340
Michigami T, Yamato H, Mushiake S et al (1996) Hypercalcemia associated with infantile fibrosarcoma producing parathyroid hormone related protein. J Clin Endocrinol Metab 81:1090–1095
Tadmor OP, Ariel I, Rabinowitz R et al (1998) Prenatal sonographic appearance of congenital fibrosarcoma. J Clin Ultrasound 26:276–279
Nonaka D, Sun CC (2004) Congenital fibrosarcoma with metastasis in a fetus. Pediatr Dev Pathol 7:187–191
Lee MJ, Cairns RA, Munk PL, Poon PY (1996) Congenital infantile fibrosarcoma: magnetic resonance imaging findings. Can Assoc Radiol J 47:121–125
Miura K, Han G, Sano M, Tsutsui Y (2002) Regression of congenital fibrosarcoma to hemangiomatous remnant with histological and genetic findings. Pathol Int 52:612–618
Madden NP, Spicer RD, Allibone EB et al (1992) Spontaneous regression of neonatal fibrosarcoma. Br J Cancer 18:S72–S75
Bourgeois JM, Knezevich SR, Mathers JA et al (2000) Molecular detection of the ETV6–NTRK3 gene fusion differentiates congenital fibrosarcoma from other childhood spindle cell tumors. Am J Surg Pathol 24:937–946
Sheng WQ, Hisaoka M, Okamoto S et al (2001) Congenital infantile fibrosarcoma: a clinicopathologic study of 10 cases and molecular detection of the ETV6–NTRK3 fusion transcripts using paraffin embedded tissues. Am J Clin Pathol 115:348–355
Rubin BP, Chen CJ, Morgan TW et al (1998) Congenital mesoblastic nephroma t(12;15) is associated with ETV6-NTRK3 gene fusion: cytogenetic and molecular relationship to congenital (infantile) fibrosarcoma. Am J Pathol 153:1451–1458
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Islam, S., Soldes, O.S., Ruiz, R. et al. Primary colonic congenital infantile fibrosarcoma presenting as meconium peritonitis. Pediatr Surg Int 24, 621–623 (2008). https://doi.org/10.1007/s00383-008-2113-0
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00383-008-2113-0