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Primary cardiac malignant peripheral nerve sheath tumor: a case report

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Abstract

Malignant peripheral nerve sheath tumors are rare sarcomas of children and adolescents, and they are aggressive tumors with a high rate of local recurrence. Here we report a case of a primary cardiac malignant peripheral nerve sheath tumor without neurofibromatosis type I. A 53-year old woman presented having had cough, expectoration, and dyspnea for 20 days and was found to have a heart-involving tumor diagnosed as a malignant peripheral nerve sheath tumor, a rare cardiac sarcoma of 9 × 4.5 × 3 cm in size. The patient underwent a successful resection of the tumor but died 14 months postoperative. We report this case for its rarity and peculiar mode of morphologic and immunohistochemical presentation.

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Authors and Affiliations

  1. Department of Pathology, Affiliated Hospital of Jining Medical University, Shandong, 272029, China

    Xiaoxia Li & Renya Zhang

  2. Department of Cardiac Surgery, Affiliated Hospital of Jining Medical University, Shandong, 272029, China

    Chaoliang Liu

Authors
  1. Xiaoxia Li
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  2. Chaoliang Liu
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  3. Renya Zhang
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Correspondence to Chaoliang Liu.

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Li, X., Liu, C. & Zhang, R. Primary cardiac malignant peripheral nerve sheath tumor: a case report. Int J Cardiovasc Imaging 35, 1615–1618 (2019). https://doi.org/10.1007/s10554-019-01608-7

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  • DOI: https://doi.org/10.1007/s10554-019-01608-7

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