Abstract
Justification
A number of guidelines are available for management of congenital heart diseases from infancy to adult life. However, these guidelines are for patients living in high income countries. Separate guidelines, applicable to Indian children, are required when recommending an intervention for congenital heart diseases, as often these patients present late in the course of the disease and may have co-existing morbidities and malnutrition.
Process
Guidelines emerged following expert deliberations at the National Consensus Meeting on Management of Congenital Heart Diseases in India, held on 10th and 11th of August 2018 at the All India Institute of Medical Sciences, New Delhi. The meeting was supported by Children’s HeartLink, a non-governmental organization based in Minnesota, USA.
Objectives
To frame evidence based guidelines for (i) indications and optimal timing of intervention in common congenital heart diseases; (ii) follow-up protocols for patients who have undergone cardiac surgery/catheter interventions for congenital heart diseases.
Recommendations
Evidence based recommendations are provided for indications and timing of intervention in common congenital heart diseases, including left-to-right shunts (atrial septal defect, ventricular septal defect, atrioventricular septal defect, patent ductus arteriosus and others), obstructive lesions (pulmonary stenosis, aortic stenosis and coarctation of aorta) and cyanotic congenital heart diseases (tetralogy of Fallot, transposition of great arteries, univentricular hearts, total anomalous pulmonary venous connection, Ebstein anomaly and others). In addition, protocols for follow-up of post surgical patients are also described, disease wise.
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References
EUROCAT Steering Committee. Congenital Heart Defect in Europe; c2014. Available from: http://www.eurocatnetwork.eu/content/EUROCATSpecialReportCHD.pdf . Accessed on Mar 05, 2019.
Hoffman JI. The global burden of congenital heart disease. Cardiovasc J Afr. 2013;24:141–5.
Bernier PL, Stefanescu A, Samoukovic G, Tchervenkov CI. The challenge of congenital heart disease worldwide: Epidemiologic and demographic facts. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2010;13:26–34.
Warnes CA. The adult with congenital heart disease: Born to be bad. J Am Coll Cardiol. 2005;46:1–8.
Working Group on Management of Congenital Heart Diseases in India. Consensus on timing of intervention for common congenital heart disease. Indian Pediatr. 2008;45:117–26.
Stout KK, Daniels CJ, Aboulhosn JA, Bozkurt B, Broberg CS, Colman JM, et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: Executive Summary: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. J Am Coll Cardiol. 2019;139:e637 97.
Tweddell JS. What do we really know about the management of patients with congenitally corrected transposition of the great arteries? J Thorac Cardiovasc Surg. 2017;154:1023–5.
Warnes CA, Williams RG, Bashore TM, Child JS, Connolly HM, Dearani JA, et al. ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease: A report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines on the management of adults with congenital heart disease). Circulation. 2008;52(23):e143–263.
Alsaied T, Alsidawi S, Allen CC, Faircloth J, Palumbo JS, Veldtman GR. Strategies for thromboprophylaxis in Fontan circulation: A meta-analysis. Heart. 2015;101:1731–7.
Van Praagh R, Van Praagh S. The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications: A study of 57 necropsy cases. Am J Cardiol. 1965;16:406–25.
Carapetis JR, Beaton A, Cunningham MW, Guilherme L, Karthikeyan G, Mayosi BM, et al. Acute rheumatic fever and rheumatic heart disease. Nat Rev Dis Primers. 2016;2:15084.
Johnson JT, Eckhauser AW, Pinto NM, Weng HY, Minich LL, Tani LY. Indications for intervention in asymptomatic children with chronic mitral regurgitation. Pediatr Cardiol. 2015;36:417–22.
Finucane K, Wilson N. Priorities in cardiac surgery for rheumatic heart disease. Glob Heart. 2013;8:213–20.
‘Nishimura RA, Otto CM, Bonow RO, Carabello BA, Erwin JP, Fleisher LA, et al. 2017 AHA/ACC focused update of the 2014 AHA/ACC guideline for the management of patients with valvular heart disease: A report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. J Am Coll Cardiol. 2017;70:252–89.
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All authors were part of the National Consensus Meeting that formulated these Guidelines. All authors reviewed the literature and drafted recommendations of respective sections assigned to them. The final document was drafted and compiled by AS and JR. All authors provided critical inputs at every stage to finalize the draft recommendations. All authors approved the final document.
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Working group on Management of Congenital Heart Disease in India., Saxena, A., Relan, J. et al. Indian Guidelines for Indications and Timing of Intervention for Common Congenital Heart Diseases: Revised and Updated Consensus Statement of the Working Group on Management of Congenital Heart Diseases. Abridged Secondary Publication. Indian Pediatr 57, 143–157 (2020). https://doi.org/10.1007/s13312-020-1733-x
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DOI: https://doi.org/10.1007/s13312-020-1733-x