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Controversies in Our Current Decade Surrounding the Management of the Adult with Congenital Heart Disease

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Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care

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Abstract

Heart defects occur in 75 of 1000 live births, 25% of which are at least moderate in severity. Less than 33% of infants born with congenital heart disease 50 years ago survived to adulthood. With current advances in pediatric cardiology and surgery, it is now estimated in developed countries that up to 95% are expected to reach adulthood. As life expectancy improves, the population of adults with congenital heart disease continues to grow. It is now estimated that the number of adults with congenital heart disease has surpassed the number of children with congenital heart disease. While this is a remarkable achievement in the field of medicine, it is now apparent that early surgical interventions were reparative, and not curative. Adults with congenital heart disease are increasingly requiring medical services and late complications are becoming increasingly apparent. As result, healthcare systems are now challenged to meet the demands of this complex and largely underserved population. This chapter discusses and highlights some of the important advances and controversies in the modern era in the management of the adult with congenital heart disease.

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Author information

Authors and Affiliations

  1. Wisconsin Adult Congenital Heart Disease Program (WAtCH), Medical College of Wisconsin, Milwaukee, WI, USA

    James Kimber, Peter Bartz, Tejas Shah & Scott Cohen

  2. Chicago Adult Congenital Heart Disease Alliance, University of Chicago Medicine, Advocate/Aurora Health Care, NorthShore University, Chicago, IL, USA

    Michael G. Earing

Authors
  1. James Kimber
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  2. Peter Bartz
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  3. Michael G. Earing
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  4. Tejas Shah
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  5. Scott Cohen
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Corresponding author

Correspondence to Scott Cohen .

Editor information

Editors and Affiliations

  1. Children’s Hospital Colorado University of Colorado Denver, School of, Aurora, CO, USA

    Eduardo M. da Cruz

  2. Children's Hospital Colorado University of Colorado School of Medicin, Aurora, CO, USA

    Dunbar Ivy

  3. Department of Cardiac Surgery, German Pediatric Heart Center, Sankt Augustin, Germany

    Viktor Hraska

  4. Pediatric Cardiac Surgery, Children's Hospital Colorado University of Colorado, Aurora, CO, USA

    James Jaggers

Section Editor information

  1. Cincinnati Children’s Hospital Medical Center, Cincinatti, OH, USA

    Gary Webb

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Kimber, J., Bartz, P., Earing, M.G., Shah, T., Cohen, S. (2023). Controversies in Our Current Decade Surrounding the Management of the Adult with Congenital Heart Disease. In: da Cruz, E.M., Ivy, D., Hraska, V., Jaggers, J. (eds) Pediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care. Springer, London. https://doi.org/10.1007/978-1-4471-4999-6_180-2

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  • DOI: https://doi.org/10.1007/978-1-4471-4999-6_180-2

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  • Print ISBN: 978-1-4471-4999-6

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