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Connective Tissue Disorder-Associated Vasculitis

  • Vasculitis (LR Espinoza, Section Editor)
  • Published:
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Abstract

Vasculitides secondary to connective tissue diseases are classified under the category of ‘vasculitis associated with systemic disease’ in the revised International Chapel Hill Consensus Conference (CHCC) nomenclature. These secondary vasculitides may affect any of the small, medium or large vessels and usually portend a poor prognosis. Any organ system can be involved and the presentation would vary depending upon that involvement. Treatment depends upon the type and severity of presentation. In this review, we describe secondary vasculitis associated with rheumatoid arthritis, systemic lupus erythematosus, sarcoidosis, relapsing polychondritis, systemic sclerosis, Sjogren’s syndrome and idiopathic inflammatory myositis, focusing mainly on recent advances in the past 3 years.

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Authors and Affiliations

  1. Department of Internal Medicine, Post Graduate Institute of Medical Education and Research, Chandigarh, India, 160012

    Aman Sharma, Aadhaar Dhooria & Ashish Aggarwal

  2. Department of Nephrology, Post Graduate Institute of Medical Education and Research, Chandigarh, India

    Manish Rathi

  3. Department of Medicine, Division of Rheumatology, & Division of Laboratory Medicine and Pathobiology, University of Toronto, Toronto, ON, Canada

    Vinod Chandran

  4. Institute of Medical Science, University of Toronto, Toronto, ON, Canada

    Vinod Chandran

  5. Centre for Prognosis Studies in the Rheumatic Diseases, Krembil Research Institute, University Health Network, Toronto, ON, Canada

    Vinod Chandran

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AS, AD, AA and MR declare that they have no conflicts of interest. VC reports grants and personal fees from AbbVie, personal fees from Amgen, personal fees from Celgene, personal fees from Janssen and personal fees from Novartis, outside the submitted work.

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Sharma, A., Dhooria, A., Aggarwal, A. et al. Connective Tissue Disorder-Associated Vasculitis. Curr Rheumatol Rep 18, 31 (2016). https://doi.org/10.1007/s11926-016-0584-x

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