Abstract
Cardiovascular involvement occurring in 20–30% patients is the second most common cause of mortality in patients with relapsing polychondritis. Aortic insufficiency occurs as a result of aortic root dilatation rather than primary valvular involvement. We are reporting a patient of relapsing polychondritis with aortic root dilatation, in whom institution of early and aggressive therapy successfully prevented the progression of aortic insufficiency.
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Sharma, A., Mittal, T., Kumar, S. et al. Successful treatment of aortic root dilatation in a patient with relapsing polychondritis. Clin Rheumatol 32 (Suppl 1), 59–61 (2013). https://doi.org/10.1007/s10067-010-1450-2
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DOI: https://doi.org/10.1007/s10067-010-1450-2