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A case of kaposiform hemangioendothelioma at the sigmoid colon

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Abstract

We report a case of kaposiform hemangioendothelioma (KHE) occurring at the sigmoid colon in an 8-year-old male. He had experienced lower abdominal pain and fever for several days. Contrast-enhanced CT images revealed a well-enhanced mass involving several large and small cystic parts with thin, enhanced walls at the sigmoid colon. The diagnosis was made histopathologically after surgical resection; the cystic parts corresponded to dilated lymphatic vessels. KHE is a rare, locally aggressive, vascular tumor that usually occurs in the soft tissues of the extremities. However, a case occurring in the bowel is extremely rare, and usually appears as bowel wall thickening. This is a unique case of KHE appearing as a mass-shaped hypervascular lesion in the bowel. Dilated lymphatic vessels in KHE may appear as a cystic part of the lesion.

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Conflict of interest

The authors declare that they have no conflict of interest.

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Authors and Affiliations

  1. Department of Radiology, Nihon University of Medicine, 30-1, Ohyaguchi Kami-cho, Itabashi-ku, Tokyo, 173-8610, Japan

    Hiroki Haradome, Yusuke Toda & Osamu Abe

  2. Department of Pediatric Surgery, Nihon University of Medicine, Tokyo, Japan

    Tsugumichi Koshinaga

  3. Department of Pathology, Nihon University of Medicine, Tokyo, Japan

    Masahiko Sugitani

Authors
  1. Hiroki Haradome
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  2. Yusuke Toda
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  3. Tsugumichi Koshinaga
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  4. Masahiko Sugitani
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  5. Osamu Abe
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Correspondence to Hiroki Haradome.

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Haradome, H., Toda, Y., Koshinaga, T. et al. A case of kaposiform hemangioendothelioma at the sigmoid colon. Jpn J Radiol 33, 494–498 (2015). https://doi.org/10.1007/s11604-015-0444-z

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  • DOI: https://doi.org/10.1007/s11604-015-0444-z

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