Abstract
Kaposiform hemangioendothelioma is a rare, highly vascular and aggressive soft tissue tumor frequently associated with Kasabach–Merritt phenomenon, usually seen in early infancy. Early diagnosis by means of MRI and tissue biopsy portends a better outcome. Treatment includes surgical excision when feasible and medical management with steroids, propranolol, vincristine and supportive treatment for coagulopathy. We report a 3 months old female infant who was diagnosed, treated successfully and is now in complete remission.
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Uppuluri, R., Kumar, V., Munirathnam, D. et al. Kaposiform Hemangioendothelioma in a 3 Months Old Infant. Indian J Hematol Blood Transfus 32 (Suppl 1), 370–371 (2016). https://doi.org/10.1007/s12288-016-0674-y
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DOI: https://doi.org/10.1007/s12288-016-0674-y