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Kaposiform Hemangioendothelioma in a 3 Months Old Infant

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Abstract

Kaposiform hemangioendothelioma is a rare, highly vascular and aggressive soft tissue tumor frequently associated with Kasabach–Merritt phenomenon, usually seen in early infancy. Early diagnosis by means of MRI and tissue biopsy portends a better outcome. Treatment includes surgical excision when feasible and medical management with steroids, propranolol, vincristine and supportive treatment for coagulopathy. We report a 3 months old female infant who was diagnosed, treated successfully and is now in complete remission.

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References

  1. Lyons LL, North PE, Lai FMM, Stoler MH, Folpe AL, Weiss SW (2004) Kaposiformhemangioendothelioma: a study of 33 cases emphasizing its pathologic, immunophenotypic, and biologic uniqueness from juvenile hemangioma. Am J Surg Pathol 28(5):559–568

    Article  PubMed  Google Scholar 

  2. Enjolras O, Breviere GM, Roger G et al (2004) Vincristine treatment for function- and life-threatening infantilehemangioma. Arch Pediatr 11:99–107

    Article  CAS  PubMed  Google Scholar 

  3. Chiu YE, Drolet BA, Blei F, Carcao M, Fangusaro J, Kelly ME et al (2012) Variable response to propranolol treatment of kaposiform hemangioendothelioma, tufted angioma, and Kasabach–Merritt phenomenon. Pediatr Blood Cancer 59(5):934–938

    Article  PubMed  PubMed Central  Google Scholar 

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Correspondence to Ramya Uppuluri.

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Uppuluri, R., Kumar, V., Munirathnam, D. et al. Kaposiform Hemangioendothelioma in a 3 Months Old Infant. Indian J Hematol Blood Transfus 32 (Suppl 1), 370–371 (2016). https://doi.org/10.1007/s12288-016-0674-y

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  • DOI: https://doi.org/10.1007/s12288-016-0674-y

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