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A spontaneously ruptured primitive neuroectodermal tumor/extraosseous Ewing’s sarcoma of the kidney with renal vein tumor thrombus

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Abstract

Primitive neuroectodermal tumor/extraosseous Ewing’s sarcoma (PNET/EES) is a childhood disease rarely seen in adults. It is a soft tissue tumor, which is often observed in the paraspinal region and lower extremity. We report the case of a 32-year-old man who presented with sudden abdominal pain on the right upper quadrant that was radiated to the right flank. During the operation, a spontaneously ruptured right kidney mass was found. The histopathologic and immunohistochemical characteristics of the excised mass were consistent with PNET/EES. This is the first known reported case of spontaneously ruptured PNET/EES of the kidney with renal vein tumor thrombus. The clinical details and the management of this case are described.

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Authors and Affiliations

  1. Surgical Department, Athens Medical Centre, Athens, Greece

    Panagiotis Moustafellos, George Athanasopoulos, Evangelia Karagianni & Evangelos Hadjiyannakis

  2. Division of General Surgery and Oncology, Royal Liverpool University Hospital, 21 Millersdale Road, Mossley Hill, L18 5HG, Liverpool, UK

    Stavros Gourgiotis

Authors
  1. Panagiotis Moustafellos
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  2. Stavros Gourgiotis
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  3. George Athanasopoulos
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  4. Evangelia Karagianni
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  5. Evangelos Hadjiyannakis
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Correspondence to Stavros Gourgiotis.

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Moustafellos, P., Gourgiotis, S., Athanasopoulos, G. et al. A spontaneously ruptured primitive neuroectodermal tumor/extraosseous Ewing’s sarcoma of the kidney with renal vein tumor thrombus. Int Urol Nephrol 39, 393–395 (2007). https://doi.org/10.1007/s11255-006-9073-x

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  • DOI: https://doi.org/10.1007/s11255-006-9073-x

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