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Atypical papillary glioneuronal tumor

  • Clinical Study–Patient Studies
  • Published:
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Abstract

We describe a 34-year-old man who presented with headaches for about 3 months. Magnetic Resonance Imaging (MRI) revealed a large cystic tumor, involving the right frontoparietal lobe region. Pathological study revealed a papillary glioneuronal tumor (PGNT) with mitotic activity and a Ki-67 labeling index of approximately 15%. Five years after radical surgery and radiotherapy, the patient is symptom-free, without tumor recurrence or residual tumor. This case supports the existence of an atypical variant of PGNT, with mitotic activity and high proliferative index, and suggests that in these tumors, histological findings of malignity not necessarily indicate a short-term unfavorable behavior.

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Authors and Affiliations

  1. Department of Neurosurgery, Puerta de Hierro Hospital, Autonomous University, San Martin de Porres, 4, Madrid, 28035, Spain

    Jesús Vaquero

  2. Department of Pathology, Central Defense Hospital, Complutensis University, Madrid, Spain

    Santiago Coca

Authors
  1. Jesús Vaquero
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  2. Santiago Coca
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Correspondence to Jesús Vaquero.

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Vaquero, J., Coca, S. Atypical papillary glioneuronal tumor. J Neurooncol 83, 319–323 (2007). https://doi.org/10.1007/s11060-007-9333-3

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  • DOI: https://doi.org/10.1007/s11060-007-9333-3

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