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Variably protease-sensitive prionopathy in a PRNP codon 129 heterozygous UK patient with co-existing tau, α synuclein and Aβ pathology

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Acknowledgments

We are grateful to the patient’s relatives for giving consent for publication of this report. This is an independent report commissioned and funded by the Policy Research Programme in the Department of Health, UK. The views expressed in the publication are those of the authors and not necessarily those of the Department of Health.

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Authors and Affiliations

  1. National CJD Surveillance Unit, School of Molecular and Clinical Medicine, The University of Edinburgh, Edinburgh, UK

    Mark W. Head, Suzanne Lowrie, Gurjit Chohan, Richard Knight & James W. Ironside

  2. Neuropathology Department, The James Cook University Hospital, Marton Road, Middlesbrough, UK

    David J. Scoones

  3. National CJD Surveillance Unit, Bryan Matthews Building, Western General Hospital, The University of Edinburgh, Edinburgh, EH4 2XU, UK

    James W. Ironside

Authors
  1. Mark W. Head
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  2. Suzanne Lowrie
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  3. Gurjit Chohan
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  4. Richard Knight
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  5. David J. Scoones
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  6. James W. Ironside
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Corresponding author

Correspondence to James W. Ironside.

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Head, M.W., Lowrie, S., Chohan, G. et al. Variably protease-sensitive prionopathy in a PRNP codon 129 heterozygous UK patient with co-existing tau, α synuclein and Aβ pathology. Acta Neuropathol 120, 821–823 (2010). https://doi.org/10.1007/s00401-010-0766-y

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  • DOI: https://doi.org/10.1007/s00401-010-0766-y

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