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Pancreaticoduodenectomy for pancreatoblastoma: a case report and literature review

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Abstract

Pancreatoblastoma (PB) is extremely rare. A 11-year-old boy, who had excision of dilated common bile duct with hepaticoduodenostomy when 9 years old was referred to our institute for further management of abdominal pain and steatorrhea. Imaging studies showed a solid 4 cm tumor in the head of the pancreas and two lesions in the liver. Needle biopsies diagnosed PB with liver metastases. After five courses of chemotherapy, the primary tumor was completely resected with pancreaticoduodenectomy (PD) and Child’s pancreaticobiliary tract reconstruction. The liver metastases were resected. Postoperative recovery was uneventful. Here, we present this case and review the literature focusing on management of PB.

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Authors and Affiliations

  1. Department of Pediatric General and Urogenital Surgery, Juntendo University School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo, 113-8421, Japan

    Rumi Ohata, Tadaharu Okazaki, Geoffrey J. Lane & Atsuyuki Yamataka

  2. Department of Hepatobiliary and Pancreatic Surgery, Juntendo University School of Medicine, Tokyo, Japan

    Yoichi Ishizaki & Seiji Kawasaki

  3. Department of Pediatrics, Juntendo University School of Medicine, Tokyo, Japan

    Junya Fujimura & Toshiaki Shimizu

Authors
  1. Rumi Ohata
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  2. Tadaharu Okazaki
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  3. Yoichi Ishizaki
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  4. Junya Fujimura
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  5. Toshiaki Shimizu
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  6. Geoffrey J. Lane
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  7. Atsuyuki Yamataka
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  8. Seiji Kawasaki
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Correspondence to Tadaharu Okazaki.

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Ohata, R., Okazaki, T., Ishizaki, Y. et al. Pancreaticoduodenectomy for pancreatoblastoma: a case report and literature review. Pediatr Surg Int 26, 447–450 (2010). https://doi.org/10.1007/s00383-010-2561-1

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  • DOI: https://doi.org/10.1007/s00383-010-2561-1

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