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Atypical teratoid rhabdoid tumor of the brain: case series and review of literature

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Abstract

Introduction

Intracranial atypical teratoid rhabdoid tumor is an uncommon malignancy with a dismal outcome. Commonly misdiagnosed over the decades as primitive neuroectodermal tumor of the brain, it has dramatically different biological behavior.

Discussion

We herein report a case series of five patients diagnosed and treated as atypical teratoid rhabdoid tumor of the brain in a major cancer center in north India. We have also analyzed the clinical, histopathological, and radiological features and the therapeutic options of this enigmatic tumor.

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Authors and Affiliations

  1. Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, New Delhi, India

    Ahitagni Biswas, Shikha Goyal, Tarun Puri, Pramod Kumar Julka & Goura Kishor Rath

  2. Department of Pathology, All India Institute of Medical Sciences, New Delhi, India

    Prasenjit Das & Chitra Sarkar

  3. Department of Medical Oncology, All India Institute of Medical Sciences, New Delhi, India

    Sameer Bakhshi

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  1. Ahitagni Biswas
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  2. Shikha Goyal
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  3. Tarun Puri
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Correspondence to Ahitagni Biswas.

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Biswas, A., Goyal, S., Puri, T. et al. Atypical teratoid rhabdoid tumor of the brain: case series and review of literature. Childs Nerv Syst 25, 1495–1500 (2009). https://doi.org/10.1007/s00381-009-0903-x

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  • DOI: https://doi.org/10.1007/s00381-009-0903-x

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