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Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature

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Abstract

Introduction

We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.

Materials and methods

Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.

Conclusion

In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.

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Notes

  1. In addition to conventional CT and MRI imaging of the head, the use of colour Doppler imaging, which can detect changes in blood flow within the orbit suggestive of canal stenosis, has been used as an additional tool when selecting patients for early or prophylactic decompression of the optic nerve [24]

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Authors and Affiliations

  1. Department of Neurosurgery, Royal Liverpool Children’s Hospital, Alder Hey, Eaton Road, Liverpool, L12 2AP, UK

    S. J. C. Sammut, J. Kandasamy, A. Sinha, J. Ross & P. May

  2. Department of Ophthalmology, Royal Liverpool Children’s Hospital, Alder Hey, Eaton Road, Liverpool, L12 2AP, UK

    W. Newman

  3. Department of Endocrinology, Royal Liverpool Children’s Hospital, Alder Hey, Eaton Road, Liverpool, L12 2AP, UK

    J. C. Blair

Authors
  1. S. J. C. Sammut
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  2. J. Kandasamy
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  3. W. Newman
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  4. A. Sinha
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  5. J. Ross
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  6. J. C. Blair
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  7. P. May
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Corresponding author

Correspondence to P. May.

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Sammut, S.J.C., Kandasamy, J., Newman, W. et al. Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature. Childs Nerv Syst 24, 515–520 (2008). https://doi.org/10.1007/s00381-007-0543-y

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  • DOI: https://doi.org/10.1007/s00381-007-0543-y

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