Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature
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- Sammut, S.J.C., Kandasamy, J., Newman, W. et al. Childs Nerv Syst (2008) 24: 515. doi:10.1007/s00381-007-0543-y
We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.
Materials and methods
Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.
In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.