Abstract
This brief report describes an observation from liver biopsy results in nonfailing Fontan patients, currently in their second postoperative decade. In three patients, with either atriopulmonary or atrioventricular connections and functional left ventricles, we found no portal fibrosis. In contrast, we found portal fibrosis in three clinically similar, nonfailing Fontan patients with lateral tunnel connections and functional left ventricles. We recognize the results may be secondary to chance; nevertheless, we speculate about possible relevancy.
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Acknowledgments
We wish to thank the interventional radiologists of Radiology Specialists at Sunrise Children’s Hospital and Medical Center, who performed the transvenous hepatic biopsies, including Drs. Demetrice Davis, Steven Davis, Kelly Gardner, Sunil Gujrathi, Aaron Peterson, and Matthew Rainey.
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Evans, W.N., Acherman, R.J., Reardon, L.C. et al. An Observation from Liver Biopsies Two Decades Post-Fontan. Pediatr Cardiol 37, 1119–1122 (2016). https://doi.org/10.1007/s00246-016-1403-x
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DOI: https://doi.org/10.1007/s00246-016-1403-x