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The turcot syndrome

Report of an additional case and review of the literature

  • Published:
Diseases of the Colon & Rectum

Abstract

Another unusual autopsy case of the Turcot syndrome is reported in a 23-year-old woman with polyposis coli, who developed primary carcinoma of the jejunum and glioblastoma multiforme of the left frontal lobe. Previously documented cases are reviewed. Discussion focuses on the occurrence of other extracolonic abnormalities observed with the Turcot syndrome

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Authors and Affiliations

  1. the Department of Neuropathology Institute of Pathology, University Hospital Eppendorf, Martinistrasse 52, D-2000, Hamburg 20, Federal Republic of Germany

    Sören Schröder M.D., Dieter Moehrs M.D., Jörg von Weltizien M.D., Rainer Winkler M.D. & Herwart F. Otto M.D.

  2. the Department of Surgery, University Hospital Eppendorf, University of Hamburg, Federal Republic of Germany

    Sören Schröder M.D., Dieter Moehrs M.D., Jörg von Weltizien M.D., Rainer Winkler M.D. & Herwart F. Otto M.D.

  3. Institute of Pathology, University Hospital Eppendorf, Martinistrasse 52, D-2000, Hamburg 20, Federal Republic of Germany

    Sören Schröder M.D., Dieter Moehrs M.D., Jörg von Weltizien M.D., Rainer Winkler M.D. & Herwart F. Otto M.D.

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  1. Sören Schröder M.D.
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  2. Dieter Moehrs M.D.
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Schröder, S., Moehrs, D., von Weltizien, J. et al. The turcot syndrome. Dis Colon Rectum 26, 533–538 (1983). https://doi.org/10.1007/BF02563749

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  • DOI: https://doi.org/10.1007/BF02563749

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