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Familial multiple polyposis coli with multiple associated tumors

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Diseases of the Colon & Rectum

Abstract

A case is described of familial polyposis of the colon, which combines almost every recorded manifestation of the syndrome of associated tumors; namely, carcinomatous changes in the polyps, osteomas of facial and other bones, periampullary carcinoma, transitional-cell carcinoma of the bladder, adrenal adenoma, intra-abdominal fibrous tumors with bowel obstruction and a remarkable tendency to contain and survive the malignancies.

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Butson, A.R.C. Familial multiple polyposis coli with multiple associated tumors. Dis Colon Rectum 26, 578–582 (1983). https://doi.org/10.1007/BF02552964

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  • DOI: https://doi.org/10.1007/BF02552964

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