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Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome

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Abstract

Alagille syndrome, or arteriohepatic dysplasia, is a disorder characterized by paucity of intrahepatic bile ducts, peculiar facies and skeletal anomalies. We report a typical case of this syndrome in an 18-year-old girl, in whom abdominal CT showed bilateral renal cysts and aortic wall calcification, findings unreported in the radiological literature.

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References

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Authors and Affiliations

  1. Department of Radiology, Hospital Juan Canalejo, Xubias de Arriba, 84, 15006, La Coruña, Spain

    F. Pombo, C. Isla, A. Gayol & A. Bargiela

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  1. F. Pombo
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  2. C. Isla
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  3. A. Gayol
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  4. A. Bargiela
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Pombo, F., Isla, C., Gayol, A. et al. Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome. Pediatr Radiol 25, 314–315 (1995). https://doi.org/10.1007/BF02011114

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  • DOI: https://doi.org/10.1007/BF02011114

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