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Large rod-like photopic signals in a possible new form of congenital night blindness

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Abstract

A 10-year-old Persian girl has symptoms of congenital stationary night blindness and some drusen-like lesions in the region of the vascular arcades. Her electroretinogram shows no rod response to a weak stimulus, but a large (475 μV) slow scotopic response to a strong stimulus that is unchanged by photopic conditions (15 F1 background illumination). However, the response to flicker had the typical (smaller) amplitude of a cone signal. This may represent a new form of night blindness in which rod sensitivity is reduced so that there is no vision under dim conditions but rod function still persists under photopic conditions.

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Authors and Affiliations

  1. Department of Ophthalmology, Stanford University School of Medicine, Stanford, California, USA

    Michael F. Marmor

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  1. Michael F. Marmor
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Marmor, M.F. Large rod-like photopic signals in a possible new form of congenital night blindness. Doc Ophthalmol 71, 265–269 (1989). https://doi.org/10.1007/BF00170975

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  • DOI: https://doi.org/10.1007/BF00170975

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