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Congenital Diaphragmatic Hernia, a Defect beyond Surgical Repair

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Intensive Care in Childhood

Part of the book series: Update in Intensive Care and Emergency Medicine ((UICM,volume 25))

Abstract

Over the years, congenital diaphragmatic hernia (CDH) has slowly, but in our days definitely, escaped the scope of surgical repair. Its high mortality, as appears now, is not caused by the anatomic defect of the diaphragm, but by a complex disorder involving hypoplasia of the lungs complicated by high resistance of the pulmonary vascular system, which leads to pulmonary hypertension, right-left shunting and ultimately to death on account of persistent serious hypoxia.

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© 1996 Springer-Verlag Berlin Heidelberg

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Molenaar, J.C. (1996). Congenital Diaphragmatic Hernia, a Defect beyond Surgical Repair. In: Tibboel, D., van der Voort, E. (eds) Intensive Care in Childhood. Update in Intensive Care and Emergency Medicine, vol 25. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-80227-0_8

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  • DOI: https://doi.org/10.1007/978-3-642-80227-0_8

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-80229-4

  • Online ISBN: 978-3-642-80227-0

  • eBook Packages: Springer Book Archive

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