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Congenital Diaphragmatic Hernia

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Pediatric Thoracic Surgery

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Abstract

Congenital diaphragmatic hernia occurs in 1–5/10,000 live births. It is characterized by a defect in the separation of the thoracic cavity from the abdominal cavity due to incomplete development of the diaphragm. It follows the herniation of abdominal viscera at the thoracic level with hypoplasia of the lung ipsilateral to the hernia. The pre- and postoperative management of the patient is very complex. Contrary to what happened in the past, surgical treatment does not necessarily have to be urgent but only under stable clinical conditions, except in special cases. The postoperative survival rate is 70–80%, up to 90% in some structures and in particular for CDH not associated with other anomalies.

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Authors and Affiliations

  1. Pediatric Surgery, IRCCS Giannina Gaslini, University of Genoa, DINOGMI, Genoa, Italy

    Girolamo Mattioli & Federico Palo

Authors
  1. Girolamo Mattioli
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  2. Federico Palo
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Correspondence to Girolamo Mattioli .

Editor information

Editors and Affiliations

  1. Department of Pediatric Surgery, IRCCS Giannina Gaslini Institute, Genova, Italy

    Girolamo Mattioli

  2. IRCCS Istituto Giannina Gaslini, Genova, Italy

    Paolo Petralia

  3. Unit of Pediatric Thoracic and Airway Surgery, IRCCS Istituto Giannina Gaslin, Genova, Italy

    Michele Torre

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Mattioli, G., Palo, F. (2021). Congenital Diaphragmatic Hernia. In: Mattioli, G., Petralia, P., Torre, M. (eds) Pediatric Thoracic Surgery. Springer, Cham. https://doi.org/10.1007/978-3-030-74668-1_18

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  • DOI: https://doi.org/10.1007/978-3-030-74668-1_18

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-74667-4

  • Online ISBN: 978-3-030-74668-1

  • eBook Packages: MedicineMedicine (R0)

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