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Fetal Left Heart Obstructive Lesions: Aortic Stenosis, Shone’s Complex, and Aortic Arch Obstruction

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Pediatric Cardiology

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Abstract

This chapter explores left-sided obstructive lesions in the fetus. This includes discussion of aortic stenosis, primarily discussing valvar stenosis with brief coverage of supravalvar aortic stenosis as well. Within this section, critical aortic stenosis and mitral valve dysplasia are discussed. The chapter goes on to include coarctation of the aorta, Shone’s complex, and interrupted aortic arch.

Within each section, we review manifestation of the lesion in obstetric ultrasound, history taking with the role of prenatal genetic testing for specific lesions as well as the role of additional testing for risk stratification and prognostication, details of fetal echocardiography, fetal life follow-up and what to expect during the remainder of the gestation, fetal interventions (if there are any), and expected changes in hemodynamics at birth with recommendations for preparation at delivery and the immediate postnatal course.

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Author information

Authors and Affiliations

  1. The Heart Center, Nationwide Children’s Hospital, Columbus, OH, USA

    Corey Stiver & Karen Texter

  2. Department of Pediatrics, The Ohio State University College of Medicine, Columbus, OH, USA

    Corey Stiver & Karen Texter

Authors
  1. Corey Stiver
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  2. Karen Texter
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Corresponding author

Correspondence to Corey Stiver .

Editor information

Editors and Affiliations

  1. Lurie Children's Hospital, Northwestern Memorial Hospital, Chicago, IL, USA

    Ra-id Abdulla

  2. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, USA

    Stuart Berger

  3. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, USA

    Carl Backer

  4. King's College, University College London, London, UK

    Robert Anderson

  5. Weill Cornell Medical College, Cornell University, New York, USA

    Ralf Holzer

  6. University of Amsterdam, Amsterdam, Noord-Holland, The Netherlands

    Nico Blom

  7. Lurie Children's Hospital of Chicago, Northwestern Memorial Hospital, Chicago, IL, USA

    Joshua Robinson

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Stiver, C., Texter, K. (2023). Fetal Left Heart Obstructive Lesions: Aortic Stenosis, Shone’s Complex, and Aortic Arch Obstruction. In: Abdulla, Ri., et al. Pediatric Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-030-42937-9_20-1

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  • DOI: https://doi.org/10.1007/978-3-030-42937-9_20-1

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-42937-9

  • Online ISBN: 978-3-030-42937-9

  • eBook Packages: Springer Reference MedicineReference Module Medicine

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