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Periorbital Bony Diseases

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Orbital Apex and Periorbital Skull Base Diseases

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Abstract

Periorbital bony diseases are rare and mostly benign. Most patients present as incidental findings, while others may complain of proptosis or visual impairment. The most common causes are benign osseous tumours such as fibrous dysplasia, meningiomas or osteomas. Malignant neoplasms such as osteosarcomas are very rare. However, tumour-like conditions like Langerhans cell histiocytosis (LCH) may occur in the orbit as a single lesion or part of a multifocal multisystem disease. Orbital LCH usually occurs in children and can be regarded as high-risk lesions for CNS involvement. Other causes in the paediatric age group can be dermoid cysts, craniosynostosis or other congenital conditions, for example, osteopetrosis and craniotubular dysplasias.

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Authors and Affiliations

  1. Department of Neurosurgery, Queen Elizabeth Hospital, Hospital Authority, Hong Kong SAR, China

    Shuk Wan Joyce Chow

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Correspondence to Shuk Wan Joyce Chow .

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  1. Department of Neurosurgery, Queen Elizabeth Hospital, Hong Kong, China

    Tak Lap POON

  2. Department of Neurosurgery, Queen Elizabeth Hospital, Hong Kong, China

    Calvin MAK

  3. Ophthalmology and Visual Sciences, Hong Kong Eye Hospital, Hong Kong, China

    Hunter Kwok Lai YUEN

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Chow, S.W.J. (2023). Periorbital Bony Diseases. In: POON, T.L., MAK, C., YUEN, H.K.L. (eds) Orbital Apex and Periorbital Skull Base Diseases. Springer, Singapore. https://doi.org/10.1007/978-981-99-2989-4_14

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  • DOI: https://doi.org/10.1007/978-981-99-2989-4_14

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