Abstract
Primary appendiceal neoplasms are rare tumors that account for approximately 1% of all cancers [1]. They are mostly found incidentally in an appendectomy specimen [1, 2]. They can also be found during abdominal imaging or during colonoscopy, as only 30–50% of patients exhibit clinical manifestations such as acute appendicitis of these tumors [3, 4]. The epidemiology of appendiceal tumors has not been established due to these clinical characteristics. A recent analysis of the Surveillance, Epidemiology, and End Results (SEER) database reported that the age-adjusted annual incidence was 6 per 1,000,000 people in recent years [3], but the incidence has increased from 2 to 4 per 1,000,000 populations in the 1970s to 5–6 per 1,000,000 in 2006–2007. The reasons for these increases are unclear but may be associated with the development of imaging tools and colonoscopy [3, 5]. In this chapter, the epidemiology and risk factors will be introduced based on previous studies (Fig. 1).
Seung Yong Shin is the lead author of this chapter.
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Chun, H.J., Park, S.J., Lim, Y.J., Song, S.Y. (2023). Epidemiology and Prevention. In: Gastrointestinal Cancer. Springer, Singapore. https://doi.org/10.1007/978-981-99-0815-8_25
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