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Mucopolysaccharides and Oligosaccharides

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Inborn Metabolic Diseases

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Abstract

Mucopolysaccharides and oligosaccharides are essential constituents of the organism. They occur in connective tissue, parenchymal organs, cartilage and the nervous system. Mucopolysaccharides (for which the preferred term is glycosaminoglycans) are complex heterosaccharides consisting of long sugar chains rich in sulphate groups. The polymeric chains are bound to specific proteins (core proteins) In glycoproteins, oligosaccharide chains are attached to a peptide core via a N-glycosidic or O-glycosidic Iinkage. There is extensive diversity in the composition and structure of oligosaccharides.

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Authors
  1. M. Beck
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  2. J. Spranger
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Editor information

Editors and Affiliations

  1. University Children’s Hospital, Oostersingel 59, 9713 EZ, Groningen, The Netherlands

    John Fernandes M.D.

  2. Hospital Necker-Enfants Malades, 149, Rue de Sèvres, 75743, Paris Cedex, France

    Jean-Marie Saudubray M.D.

  3. International Institute of Cellular and Molecular Pathology, Avenue Hippocrate 75, 1200, Brussels, Belgium

    Georges Van den Berghe M.D.

  4. Sendai, Japan

    K. Tada

  5. Portland, Oregon, USA

    N. R. M. Buist

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© 1995 Springer-Verlag Berlin Heidelberg

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Beck, M., Spranger, J. (1995). Mucopolysaccharides and Oligosaccharides. In: Fernandes, J., Saudubray, JM., Van den Berghe, G., Tada, K., Buist, N.R.M. (eds) Inborn Metabolic Diseases. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-03147-6_36

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  • DOI: https://doi.org/10.1007/978-3-662-03147-6_36

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-03149-0

  • Online ISBN: 978-3-662-03147-6

  • eBook Packages: Springer Book Archive

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