Retinoblastoma Management: Connecting Institutions with Telemedicine

Chapter

Abstract

Retinoblastoma is a malignant pediatric eye tumor that is highly curable if the disease remains intraocular; its cure rate and sight preservation rate exceeds 90% in developed countries in part because of early diagnosis and access to adequate treatment. Retinoblastoma accounts for approximately 3% of all pediatric malignancies, and approximately two-thirds of patients present with unilateral disease, while one-third have bilateral involvement. Patients with unilateral disease are usually treated with enucleation, while few also receive adjuvant chemotherapy or radiation therapy. Management of bilateral patients is much more challenging since eye salvage and vision preservation must also be considered. The management of these cases includes chemotherapy and careful, intensive use of focal treatments. Such a regimen therefore requires the cooperation of a highly specialized, multidisciplinary team.

Keywords

Outreach Program Grand Round Unilateral Disease Catastrophic Illness Transpupillary Thermotherapy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Notes

Acknowledgments

United States

Eugene Helveston, M.D.

Ophthalmologist-in-Chief

ORBIS International

Al L. Ueltschi

Chairman

ORBIS International & FlightSafety International, Inc.

Lynda Smallwood

Senior Manager, Cyber-Sight

ORBIS International

Matthew W. Wilson, M.D., FACS

Professor of Ophthalmology

UT Hamilton Eye Institute

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

James C. Fleming, M.D., FACS

Philip M. Lewis Professor of Ophthalmology

Director of the Orbit Center

Hamilton Eye Institute

UT Health Science Center

Memphis, TN

Raul C. Ribeiro, M.D.

Director, Leukemia/Lymphoma

Director, International Outreach

St. Jude Children’s Research Hospital, Memphis, TN

Judith A. Wilimas, M.D.

Medical Director

Referring Physicians Office and Domestic Affiliate Program

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Carlos Rodriguez-Galindo, M.D.

Pediatric Oncologist

Dana-Farber Cancer Institute/

Children’s Hospital Boston

Boston, MA

Ibrahim Qaddoumi, M.D., M.S.

Director of Telemedicine

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

George Vélez, DHAc, M.B.A., CFAAMA

Administrative Director

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Gaston K. Rivera, M.D.

Medical Director, Chile Program

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Yuri Quintana, Ph.D.

Director, Education and Informatics

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Richard O’Brien

Educational Technologies Administrator

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Jorge I. Calzada, M.D.

Ophthalmologist

Hamilton Eye Institute

UT Health Science Center

Memphis, TN

Sandra Luna-Fineman, M.D.

Pediatric Hematologist/Oncologist

California Pacific Med Center-Davies

San Francisco, CA

The Richard T. and Josephine Arkwright Foundation

New York, NY

Robert B. Carter, M.B.A.

Executive Vice President & Chief Information Officer

FedEx Corporation

Memphis, TN

Blanca Phillips

Coordinator and Ophthalmic Photographer

UT Hamilton Eye Institute

International Outreach Program

St. Jude Children’s Research Hospital

Memphis, TN

Lee A. Thompson, M.A.

Publication Specialist

Hamilton Eye Institute

UT Health Science Center

Memphis, TN

Guatemala

Federico Antillon-Klussman, M.D.

Pediatric Hematologist/Oncologist & Medical Director

Hospital de Oncología Pediátrica

Guatemala City, Guatemala

Margarita Barnoya, M.D.

Ophthalmologist

Hospital de Oncología Pediátrica

Guatemala City, Guatemala

Mauricio Castellanos, M.D.

Pediatric Hematologist/Oncologist

Hospital de Oncología Pediátrica

Guatemala City, Guatemala

Guillermo Chantada, M.D.

Pediatric Hematologist/Oncologist

Department of Hemato-Oncology, Hospital JP Garrahan

Buenos Aires, Argentina

Panama

Ernesto Calvo, M.D.

Ophthalmologist

Clinica de Ojos Orillac-Calvo

Panama, Republic of Panama

Maria Sabina Ahchu, M.D.

Pediatric Hematologist/Oncologist

Hospital del Niño de Panamá

Panama, Republic of Panama

J. Thomas Ford

Trustee, Board Member

Director, and Past President Programa Niños Sanos: Niños Felices

Panama, Republic of Panama

Honduras

Ligia Fu, M.D.

Pediatric Hematologist/Oncologist & Medical Director

Hospital Escuela Materno Infantil

Tegucigalpa, Honduras

Carlos Maldonado, M.D.

Ophthalmologist

Hospital Escuela Materno Infantil

Tegucigalpa, Honduras

Lilia Lopez, M.D.

Ophthalmologist

Hospital Escuela Materno Infantil

Tegucigalpa, Honduras

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Copyright information

© Springer-Verlag Berlin Heidelberg 2012

Authors and Affiliations

  1. 1.Department of OphthalmologyCollege of Medicine, UT Health Science Center, UT Hamilton Eye InstituteMemphisUSA
  2. 2.Division of Ophthalmology, Department of SurgerySt. Jude Children’s Research HospitalMemphisUSA

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