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Lymphknoten bei angeborenen Immundefekten

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Pathologie

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Zusammenfassung

Dieses Kapitel gibt eine kurzgefasste Übersicht über die zahlreichen angeborenen Immundefekte, der Zahl vor dem Hintergrung der kompletten genetischen Analysen durch NGS ständig zunimmt. Die wichtigsten Klassen werden vorgestellt und einige Syndrome und Befunde, die in der täglichen Diagnostik auftreten und an Lymphknotenveränderungen diagnostiziert oder zumindest in der Differenzialdiagnose erwähnt werden sollten, ausführlich und detailliert beschrieben. Hierzu zählen das Antikörpermangel Syndrom, das autoimmune lymphoproliferative Syndrom, die hämophagozytische Lymphohistiozytose, die chronische infantile Granulomatose und genetische Dispositionen für bestimmte Erreger wie EBV und Tuberkulose.

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Authors and Affiliations

  1. Pathologisches Institut der Universität Würzburg, Würzburg, Deutschland

    Prof. Dr. Dr. h.c. Hans Konrad Müller-Hermelink

  2. Städt. Klinikum Karlsruhe, Karlsruhe, Deutschland

    Prof. Dr. Thomas Rüdiger

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  1. Prof. Dr. Thomas Rüdiger
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Correspondence to Hans Konrad Müller-Hermelink .

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Editors and Affiliations

  1. der Universität Würzburg, Pathologisches Institut der Universität Würzburg, Würzburg, Bayern, Germany

    Hans Konrad Müller-Hermelink

  2. Medizinische Hochschule Hannover (MHH) Inst. Pathologie, Hannover, Germany

    Hans H. Kreipe

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Müller-Hermelink, H.K., Rüdiger, T. (2019). Lymphknoten bei angeborenen Immundefekten. In: Müller-Hermelink, H., Kreipe, H. (eds) Pathologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-85184-4_21

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  • DOI: https://doi.org/10.1007/978-3-540-85184-4_21

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  • Print ISBN: 978-3-540-85183-7

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