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Vascular Disorders of the Liver

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Textbook of Pediatric Gastroenterology, Hepatology and Nutrition

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Abstract

Hepatic vascular abnormalities are, at least in their primary form, rare in infants and children. Vascular disorders of the liver can be grouped according to whether the blood flow towards, into, or from the liver is affected. Based on this classification, we consecutively discuss portal vein and hepatic artery abnormalities (inflow), disturbances of the sinusoidal blood flow (e.g. peliosis hepatis), and anomalies in hepatic venous outflow such as seen in Budd–Chiari syndrome (BCS) and veno-occlusive disease. A separate section on vascular shunts reviews hepatic arteriovenous malformations and portosystemic shunts. Furthermore, nodular regenerative hyperplasia (NRH) and focal nodular hyperplasia (FNH) are addressed in a section on parenchymal responses to vascular injury. The final part of this chapter focusses on vascular tumours in the liver.

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Authors and Affiliations

  1. Department of Pediatric Gastroenterology, Hepatology and Nutrition, Ghent University Hospital, Ghent, Belgium

    Ruth De Bruyne

  2. Department of Pediatric Gastroenterology, Sophia Children’s Hospital, Erasmus Medical Center, Rotterdam, The Netherlands

    Pauline De Bruyne

  3. Department of Internal Medicine and Pediatrics, Ghent University, Ghent, Belgium

    Pauline De Bruyne

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  1. Section of Pediatric Gastroenterology Hepatology and Nutrition, University of Chicago, Chicago, IL, USA

    Stefano Guandalini

  2. Pediatric Liver, GI and Nutrition Center, Child Health, King’s College Hospital, London, UK

    Anil Dhawan

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De Bruyne, R., De Bruyne, P. (2022). Vascular Disorders of the Liver. In: Guandalini, S., Dhawan, A. (eds) Textbook of Pediatric Gastroenterology, Hepatology and Nutrition. Springer, Cham. https://doi.org/10.1007/978-3-030-80068-0_70

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