Ear, Nose, and Throat Problems and Hearing Abnormalities

  • Don C. Van Dyke
  • Maurice E. Popejoy
  • William G. Hemenway
Part of the Disorders of Human Learning, Behavior, and Communication book series (HUMAN LEARNING)


Ear, nose, oral, pharyngeal, and hearing problems are frequent areas of concern in children with Down syndrome. From a management standpoint, recurrent ear infections with associated hearing loss, chronic sinusitis with rhinorrhea, and ear wax impaction are frequent primary care concerns and often require long-term medical intervention and follow-up. Frequently reported anomalies of the palate, midface, and external auditory canals often involve both medical and surgical management issues.


Hearing Loss Down Syndrome Otitis Medium Tympanic Membrane External Auditory Canal 
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  1. Aase, J.M., Wilson, A.C., & Smith, D.W. (1973). Small ears in Down’s syndrome: A helpful diagnostic aid. Journal of Pediatrics, 82 (5), 845–847.PubMedCrossRefGoogle Scholar
  2. American Speech, Hearing and Language Association (ASHA). (1979). Guidelines for determining the threshold level of speech, Journal of American Speech, Language and Hearing Association, 21 (5), 353–356.Google Scholar
  3. Balkany, T.J., Downs, M.P., Jafek, B.W., & Krajicek, M.J. (1979). Hearing loss in Down’s syndrome: A treatable handicap more common than generally recognized. Clinical Pediatrics, 18(2), 116–118.PubMedCrossRefGoogle Scholar
  4. Balkany, T.J., Mischke, R.E., Downs, M.P., & Jafek, B.W. (1979). Ossicular abnormalities in Down’s syndrome. Otolaryngology Head and Neck Surgery, 87, 372–384.Google Scholar
  5. Brooks, D.N., Wooley, A., & Kanjilal, G.C. (1972). Hearing loss and middle ear disorders in patients with Down’s syndrome (Mongolism). Journal of Mental Deficiency Research, 16, 21.PubMedGoogle Scholar
  6. Dahle, A.J., & McCollister, F.P. (1986). Hearing and otologic disorders in children with Down’ syndrome. American Journal of Mental Deficiency, 90, 636–642.PubMedGoogle Scholar
  7. Downs, M.P. (1977). The expanding imperatus of early identification. Childhood deafness: Causation, assessment and management, F.H. Bess (Ed.), New York: Grune & Stratton.Google Scholar
  8. Downs, M.P., Jafek, B.W., & Wood, II, R.P. (1981). Comprehensive treatment of children with recurrent serous otitis media. Otolaryngology Head and Neck Surgery, 89, 658–665.PubMedGoogle Scholar
  9. Fulton, R., & Lloyd, L. (1968). Hearing impairment in a population of children with Down’s syndrome. American Journal of Mental Deficiency, 73, 298–302.PubMedGoogle Scholar
  10. Glovsky, L. (1966). Audiological assessment of a mongoloid population. Training School Bulletin, 33, 37.Google Scholar
  11. Grundfast, K.M., & Camilon, F. (1986). External auditory canal stenosis in palatal atresia without associated anomalies. Annals of Otorhinolaryngology, 95, 505–509.Google Scholar
  12. Holm, V., & Kunze, L. (1969). Effect of chronic otitis media on language and speech development. Pediatrics, 43, 883.Google Scholar
  13. Kavanagh, K.T., Kahane, K.C., & Kordan, B. (1986). Risk and benefits of adenotonsilectomy for children with Down’s syndrome. American Journal of Mental Deficiency, 91 (1), 22–29.Google Scholar
  14. Keiser, H., Montague, J., Wold, D., Maune, S., & Pattison, S.M. (1981). Hearing loss of Down syndrome adults. American Journal of Mental Deficiency, 85 (5), 467–472.PubMedGoogle Scholar
  15. Kessner, D.M., Snow, C.K., & Singer, J. (1974). Assessment of medical care for children. Contrasts in Health Status Vol. III. Washington, D.C.: National Academy of Science.Google Scholar
  16. Levinson, A., Friedman, A., & Stamps, F. (1955). Variability of Mongolism. Pediatrics, 16, 43.PubMedGoogle Scholar
  17. Maurizi, M., Ottaviani, F., Paludetti, G., & Lungarotti, S. (1985). Audiological findings in Down’s syndrome. International Journal of Pediatric Otorhinolaryngology, 9, 227–232.PubMedCrossRefGoogle Scholar
  18. Northern, J.L., & Downs, M.P. (1984). Hearing in children, 3d ed. Baltimore, Md.: Williams and Wilkins.Google Scholar
  19. Paludetti, G., Maurizi, M., Altissimi, G., Frenguelli, A., Ottaviani, F., & Rosignolli, M. (1979). L’audiometria del tronco dell’ encefalo in alcuni tipi di ipoacusieperifericche. Nuovo Arch It Otol., 7, 519–542.Google Scholar
  20. Redman, R.S., Shapiro, B.L., & Gorlin, R.J. (1965). Measurement of normal and reportedly malformed palatal vaults III, Down syndrome (trisomy 21, mongolism). Journal of Pediatrics, 67 (2), 162–165.CrossRefGoogle Scholar
  21. Samuelson, M.E., & Nguyen, V.T. (1980). Middle ear effusion in Down’s syndrome patients. Nebraska Medical Journal, 65 (4), 83–84.PubMedGoogle Scholar
  22. Schendel, S.A., & Gorlin, R.J. (1974). Frequency of cleft uvula and submucous cleft in patients with Down’s syndrome. Journal of Dental Research, 53(4), 840–843.PubMedCrossRefGoogle Scholar
  23. Schwartz, D.M., & Schwartz, R.H. (1978). Acoustic impedance and otoscopic findings in children with Down’s syndrome. Archives of Otolaryngology, 104(11), 652–656.PubMedCrossRefGoogle Scholar
  24. Strome, M. (1981). Down’s syndrome: A modern otorhinolaryngological perspective. The Laryngoscope, 91 (10), 1581–1594.PubMedCrossRefGoogle Scholar
  25. Walby, A.P., & Schuknecht, H.F. (1984). Concomitant occurrence of cochleoccular dysplasia in Down’s syndrome. Archives of Otolaryngology, 110(7), 447–479.CrossRefGoogle Scholar

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© Springer-Verlag New York Inc. 1990

Authors and Affiliations

  • Don C. Van Dyke
  • Maurice E. Popejoy
  • William G. Hemenway

There are no affiliations available

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