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Diagnosis and Treatment of Congenital Sensorineural Hearing Loss

  • Pediatric Otolaryngology (K Rosbe, Section Editor)
  • Published:
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Abstract

Purpose of Review

The aim of this report is to review current literature regarding the work-up and management of congenital sensorineural hearing loss.

Recent Findings

Diagnostic evaluation of a newborn with sensorineural hearing loss begins with a complete audiologic evaluation and comprehensive history and physical exam. This review presents a diagnostic algorithm for the work-up of congenital hearing loss, focusing on the three following modalities: cytomegalovirus testing, genetic evaluation, and imaging.

Summary

Newborn hearing loss is a common problem and may be attributed to genetic and non-genetic factors. Complete diagnostic evaluation and treatment are essential for preventing delays in language development. Treatment consists of early intervention services and consideration of hearing aid amplification and cochlear implantation.

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Authors and Affiliations

  1. Department of Otolaryngology—Head and Neck Surgery, University of California San Francisco, 2233 Post Street, San Francisco, CA, 94115, USA

    Divya A. Chari & Dylan K Chan

Authors
  1. Divya A. Chari
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  2. Dylan K Chan
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Correspondence to Dylan K Chan.

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The authors declare that they have no conflict of interest.

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This article does not contain any studies with human or animal subjects performed by any of the authors.

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This article is part of the Topical Collection on Pediatric Otolaryngology

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Chari, D.A., Chan, D.K. Diagnosis and Treatment of Congenital Sensorineural Hearing Loss. Curr Otorhinolaryngol Rep 5, 251–258 (2017). https://doi.org/10.1007/s40136-017-0163-3

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  • DOI: https://doi.org/10.1007/s40136-017-0163-3

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