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Successful surgical repair of d-transposition of the great arteries in a separated conjoined twin

  • Case Report
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Abstract

Abstract

Conjoined twins are very rare examples of congenital malformations. In 75% of thoracoomphalopagus conjoined twins, the intracardiac anatomy determines outcome and long-term survival.

Methods

We successfully separated one case of thoraco-omphalopagus conjoined twins, with one having d-transposition of the great arteries. After control of sepsis, the twin underwent an arterial switch and complete repair of her cardiac defect.

Results

She made a full recovery and was discharged from the hospital 20 days after surgery.

Conclusion

Careful planning, skillful surgical separation and cardiac surgery by a combined medical and surgical team is the key to save the twins in such a rare case.

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Authors and Affiliations

  1. Children’s Heart Center, Children’s Hospital of Fudan University, Shanghai, 201102, China

    Gang Chen, Bing Jia & Wen-Bo Zhang

  2. 399 Wanyuan Road, Shanghai, 201102, China

    Bing Jia

Authors
  1. Gang Chen
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  2. Bing Jia
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  3. Wen-Bo Zhang
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Corresponding author

Correspondence to Bing Jia.

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Chen, G., Jia, B. & Zhang, WB. Successful surgical repair of d-transposition of the great arteries in a separated conjoined twin. World J Pediatr 8, 371–373 (2012). https://doi.org/10.1007/s12519-012-0385-x

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  • DOI: https://doi.org/10.1007/s12519-012-0385-x

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